Abstract:
Objective
To investigate the clinical characteristics，treatment and prognosis of primary renal angiosarcoma （PRA）.
Methods
One case of primary renal angiosarcoma complicated with hemorrhage and multiple systemic metastases was retrospectively analysed and relevant literatures were reviewed.
Results
The patient was admitted to our hospital for “acute left abdominal pain for 5 hours”，CT revealed a tumor in his left kidney complicated with hemorrhage，palliative left nephrectomy was performed and pathologic diagnosis confirmed renal angiosarcoma，though chemotherapy，targeted therapy and immunotherapy were carried out.The patient's condition was stable during treatment.After 3 courses of comprehensive treatment，the patient gave up for economic reasons，and dead one-year after operation.
Conclusions
Primary renal angiosarcoma is an exceedingly rare and highly aggressive neoplasm with a poor prognosis，the final diagnosis depends on pathology.Once diagnosed，radical nephrectomy should be performed early，chemotherapy and radiotherapy should be followed after surgery，targeted therapy and immunotherapy may be effective treatments for PRA.
Key words:
Kidney,
Primary,
Angiosarcoma,
Diagnosis and treatment
Yang Wang, Nan Zhang, Weifeng Yang, Haitian He, Kebing Wang. Primary renal angiosarcoma complicated with hemorrhage: a case report and literature review[J]. Chinese Journal of Endourology(Electronic Edition), 2025, 19(02): 248-249.